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When you enter multiple keywords separated by space, your search will contain results that match any of the keywords (OR search).
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17 Hits
Search Condition : Filter (MeSH = Motor Neurons / pathology)
Species
Resource
RRC ID
Title
Journal
Published
Link
Mice
RBRCGD000108
,
RBRCGD000110
72270
Mice with endogenous TDP-43 mutations exhibit gain of splicing function and characteristics of amyotrophic lateral sclerosis.
EMBO J
2018-6-1
Pubmed
Full text
Human and Animal Cells
409B2(HPS0076)
69751
A widespread family of heat-resistant obscure (Hero) proteins protect against protein instability and aggregation.
PLoS Biol
2020-3-1
Pubmed
Full text
C.elegans
tm700
65175
Disruption of genes associated with Charcot-Marie-Tooth type 2 lead to common behavioural, cellular and molecular defects in Caenorhabditis elegans.
PLoS One
2020-1-1
Pubmed
Full text
Zebrafish
Tg(isl1:GFP)rw0
64806
Exosc2 deficiency leads to developmental disorders by causing a nucleotide pool imbalance in zebrafish.
Biochem Biophys Res Commun
2020-12-17
Pubmed
Full text
Zebrafish
Tg(HuC:GVP)
59925
Myelin degeneration induced by mutant superoxide dismutase 1 accumulation promotes amyotrophic lateral sclerosis.
Glia
2019-10-1
Pubmed
Full text
Mice
RBRC02192
,
RBRC05147
57665
Involvement of p38 in Age-Related Decline in Adult Neurogenesis via Modulation of Wnt Signaling.
Stem Cell Reports
2019-6-11
Pubmed
Full text
Drosophila
57169
Hippo, Drosophila MST, is a novel modifier of motor neuron degeneration induced by knockdown of Caz, Drosophila FUS.
Exp Cell Res
2018-10-15
Pubmed
Full text
C.elegans
tm1086
54300
The C. elegans BRCA2-ALP/Enigma Complex Regulates Axon Regeneration via a Rho GTPase-ROCK-MLC Phosphorylation Pathway.
Cell Rep
2018-8-14
Pubmed
Full text
C.elegans
tm4255
53279
Neuron-specific knock-down of SMN1 causes neuron degeneration and death through an apoptotic mechanism.
Hum Mol Genet
2016-6-15
Pubmed
Full text
Drosophila
6117R-1
,
6117R-2
50062
The PKA-C3 catalytic subunit is required in two pairs of interneurons for successful mating of Drosophila.
Sci Rep
2018-2-6
Pubmed
Full text
Zebrafish
Tg(CM-isl1:GFP)
49692
Altered RNA metabolism due to a homozygous RBM7 mutation in a patient with spinal motor neuropathy.
Hum Mol Genet
2016-7-15
Pubmed
Full text
DNA material
pEF-BOS FLAG-mouse Rab29 (RDB14971)
,
pEF-BOS FLAG-mouse Rab29-Q67L (RDB14972)
,
pEF-BOS FLAG-mouse Rab29-T21N (RDB14973).
48779
C9orf72 and RAB7L1 regulate vesicle trafficking in amyotrophic lateral sclerosis and frontotemporal dementia.
Brain
2017-4-1
Pubmed
Full text
C.elegans
tm2484
45652
Neurodegeneration in C. elegans models of ALS requires TIR-1/Sarm1 immune pathway activation in neurons.
Nat Commun
2015-6-10
Pubmed
Full text
Zebrafish
Tg(brn3a-hsp70:GFP)/rw0110b
39997
The cellular and molecular progression of mitochondrial dysfunction induced by 2,4-dinitrophenol in developing zebrafish embryos.
Differentiation
2015-1-1
Pubmed
Full text
Zebrafish
Tg(isl1:GFP)/
rw0
33660
Early interneuron dysfunction in ALS: insights from a mutant sod1 zebrafish model.
Ann Neurol
2013-2-1
Pubmed
Full text
C.elegans
tm2815
6437
The function of a spindle checkpoint gene bub-1 in C. elegans development.
PLoS One
2009-6-15
Pubmed
Full text
Human and Animal Cells
GI-1(RCB0763)
1257
VEGF is a modifier of amyotrophic lateral sclerosis in mice and humans and protects motoneurons against ischemic death.
Nat Genet
2003-8-1
Pubmed
Full text