RRC ID 1527
Author Maeda T, Yagasaki F, Ishikawa M, Takahashi N, Bessho M.
Title Transforming property of TEL-FGFR3 mediated through PI3-K in a T-cell lymphoma that subsequently progressed to AML.
Journal Blood
Abstract We previously reported a novel fusion between TEL and FGFR3 in a patient with peripheral T-cell lymphoma with t(4; 12)(p16;p13). Disease in this patient subsequently progressed to acute myelogenous leukemia (AML) with the same translocation. Sequence analysis of TEL-FGFR3 fusion transcripts suggested that these diseases originated from the same multipotent stem cell. To determine the transforming property of TEL-FGFR3, we established transfectants of this chimeric fusion gene and investigated the major signal pathways of TEL-FGFR3-induced transformation using various signal transduction inhibitors including SU5402 (fibroblast growth factor tyrosine kinase [FGFR TK] inhibitor). Our results indicated that (1) the expression of TEL-FGFR3 but not DeltaHLH-TEL-FGFR3 resulted in efficient focus formation in NIH/3T3 cells and conferred interleukin 3 independence to Ba/F3 cells by a constitutive tyrosine kinase activity probably through oligomerization by the HLH domain of TEL; (2) although effector proteins including classical mitogen-activated protein kinase (MAPK), p38 MAPK, phosphatidylinositol 3-kinase (PI3-K), mammalian target or rapamycin (mTOR), signal transducer and activator of transcription 3 (STAT-3) and STAT-5 were activated in TEL-FGFR3 transformants, the growth of the transformants was inhibited by SU5402 (concentration that inhibits 50% [IC5)]=5 microM) and the PI3-K inhibitor, LY294002 (IC5)=10 microM) and wortmannin (IC50=5 microM), but not by U0126, SB203580, or rapamycin; and (3) injection of TEL-FGFR3 transformants induced lethal leukemia into syngeneic mice. Taken together, the leukemogenic potential of TEL-FGFR3 may be mediated in part through PI3-K.
Volume 105(5)
Pages 2115-23
Published 2005-3-1
DOI 10.1182/blood-2003-12-4290
PII S0006-4971(20)45825-2
PMID 15514005
MeSH Acute Disease Animals Cell Line Cell Proliferation Cell Transformation, Neoplastic* Disease Progression Female Humans Leukemia, Myeloid / etiology* Lymphoma, T-Cell / pathology* Mice Middle Aged Oncogene Proteins, Fusion / genetics Oncogene Proteins, Fusion / physiology* Phosphatidylinositol 3-Kinases / metabolism* Receptor, Fibroblast Growth Factor, Type 3 Signal Transduction Transfection
IF 17.794
Times Cited 24
WOS Category HEMATOLOGY
Altmetric score
オルトメトリクス指標項目
The most frequently cited source Patent(IFI CLAIMS)
Total number of mentions 43
Altmetric score changes over past 6months 0.0
Resource
Human and Animal Cells Ba/F3(RCB0805)