Staff Login
Japanese
| English
Contact Us
List
Search
Browse
Registration
Statistics
Search
Home
List
Detail
Reference - Detail
RRC ID
76097
Author
Yang Q, Liu P, Anderson NS, Shpilka T, Du Y, Naresh NU, Li R, Zhu LJ, Luk K, Lavelle J, Zeinert RD, Chien P, Wolfe SA, Haynes CM.
Title
LONP-1 and ATFS-1 sustain deleterious heteroplasmy by promoting mtDNA replication in dysfunctional mitochondria.
Journal
Nat Cell Biol
Volume
24(2)
Pages
181-193
Published
2022-2-1
DOI
10.1038/s41556-021-00840-5
PII
10.1038/s41556-021-00840-5
PMID
35165413
PMC
PMC8868506
MeSH
ATP-Dependent Proteases* / genetics
ATP-Dependent Proteases* / metabolism
Animals
Animals, Genetically Modified
Caenorhabditis elegans* / genetics
Caenorhabditis elegans* / metabolism
Caenorhabditis elegans Proteins* / genetics
Caenorhabditis elegans Proteins* / metabolism
Cell Line
DNA Polymerase gamma / genetics
DNA Polymerase gamma / metabolism
DNA Replication*
DNA, Mitochondrial* / biosynthesis
DNA, Mitochondrial* / genetics
Heteroplasmy*
Humans
Mitochondria* / genetics
Mitochondria* / metabolism
Mitochondria* / pathology
Mitochondrial Proteins* / genetics
Mitochondrial Proteins* / metabolism
Oxidative Phosphorylation*
Proteolysis
Transcription Factors* / genetics
Transcription Factors* / metabolism
Resource
C.elegans
tm598