RRC ID 75991
著者 Kropp PA, Wu J, Reidy M, Shrestha S, Rhodehouse K, Rogers P, Sack MN, Golden A.
タイトル Allele-specific mitochondrial stress induced by Multiple Mitochondrial Dysfunctions Syndrome 1 pathogenic mutations modeled in Caenorhabditis elegans.
ジャーナル PLoS Genet
巻・号 17(8)
ページ e1009771
公開日 2021-8-1
DOI 10.1371/journal.pgen.1009771
PII PGENETICS-D-21-00475
PMID 34449775
PMC PMC8428684
MeSH Alleles Animals Caenorhabditis elegans / genetics Caenorhabditis elegans Proteins / genetics Carrier Proteins / genetics Carrier Proteins / metabolism Disease Models, Animal Iron / metabolism Iron-Sulfur Proteins / genetics* Iron-Sulfur Proteins / metabolism* Mitochondria / genetics Mitochondrial Diseases / genetics* Mitochondrial Diseases / physiopathology Mitochondrial Proteins / genetics Mutation Phenotype Protein Conformation Protein Multimerization Stress, Physiological / genetics Sulfur / metabolism
リソース情報
線虫 tmC5